Poems Syndrome in A-10-year-old Gi̇rl: a Case Report Poems Sendromu: 10 Yaşinda Kiz Olgu
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چکیده
POEMS syndrome has been defined as an association of plasma celi dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein and skin changes. In this report, we describe a case of POEMS syndrome. A 10-year-old girl presented with polyneoropathy, diabetes mellitus type I, double monoclonal gammopathy (IgA and IgG), hepatomegaly, cardiomegaly, hyperpigmentation, and hypertricosis. To our knowledge, she is the youngest case of POEMS syndrome who has been reported.
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